Meningioangiomatosis: a rare presentation with progressive cortical blindness.

نویسندگان

  • Akshay Shah
  • Daniel Korya
  • Brandon T Larsen
  • Myrka Torres
  • Kendra Drake
  • John La Wall
چکیده

A 58-year-old man presented with a 6-month history of headaches, progressive left homonymous hemianopia, and right-sided paresthesias. MRI revealed bilateral parietal and occipital enhancing lesions (figure 1, A–C) suggestive of cerebritis or posterior reversible encephalopathy syndrome due to history of hypertension. Worsening vision prompted neuroimaging 18 months later, showing contrast-enhancing cortical lesions in the posterior frontal region; fluid-attenuated inversion recovery abnormalities in the white matter (figure 1, D–F) suggested vasogenic edema and mass effect. Occipital lobe biopsy revealed cortical mesenchymal capillary proliferation typical of meningioangiomatosis (figure 2), a rare benign progressive disorder characterized by cortical vascular proliferation with associated perivascular mesenchymal cell proliferation. Seizures are the presenting feature in 85% of sporadic cases; there have been no reports with permanent focal dysfunction as in this instance.

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عنوان ژورنال:
  • Neurology

دوره 81 5  شماره 

صفحات  -

تاریخ انتشار 2013